Hereditary hemorrhagic telangiectasia with lung arteriovenous malformation

By
  • Dr Antoine Micheau

Publication date: September 13, 2011 | Updated on June 9, 2015

Report

Diagnosis

Hereditary hemorrhagic telangiectasia with lung arteriovenous malformation

History

Acute hemopthysis since 5 days on a 16 yo boy.

Spontaneous recurrent epistaxis in childhood

Findings

CT :

Multiple arterioveinous malformations (AVM) in right and left lung.

The biggest AVM is located on left upper lobe, with enlarged feeding artery and draining vein.

Lung angiography :

Pulmonary AVMs with single artery draining into an enlarged vein. Embolization with detachable metal coils.